We describe two cases of Reactive Hemophagocytic syndrome (RHS) occurring in rheumatic diseases in childhood. Patient 1, an adolescent girl with systemic onset Juvenile idopathic arthritis (JRA) presented like severe sepsis with shock, hepatic dysfunction and coagulopathy. Patient 2 presented with cardiac tamponade, she was later detected to have systemic lupus erythematosus (SLE). Her bone marrow aspirate revealed prominent hemophagocytosis. Both cases improved with pulse methylprednisolone therapy.
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King Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi ArabiaKing Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi Arabia
Owaidah, TM
Khalil, SH
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King Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi ArabiaKing Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi Arabia
Khalil, SH
Mustafa, MM
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King Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi ArabiaKing Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi Arabia
Mustafa, MM
Ayas, M
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King Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi ArabiaKing Faisal Specialist Hosp & Res Ctr, Dept Pathol & Lab Med MBC10, Riyadh 11211, Saudi Arabia