Reactive Hemophagocytic syndrome

被引：0
|
作者：
L. Rajam
Vinitha Prasad
B.L. Yatheesha
机构：
[1] Amrita Institute of Medical Sciences and Research Center,Department of Pediatrics
[2] Amrita Institute of Medical Sciences and Research Centre,undefined
来源：
The Indian Journal of Pediatrics | 2008年 / 75卷
关键词：
Reactive hemophagocytic syndrome; Acute lupus hemophagocytic syndrome; Cardiac tamponade;
D O I：
暂无
中图分类号：
学科分类号：
摘要：
We describe two cases of Reactive Hemophagocytic syndrome (RHS) occurring in rheumatic diseases in childhood. Patient 1, an adolescent girl with systemic onset Juvenile idopathic arthritis (JRA) presented like severe sepsis with shock, hepatic dysfunction and coagulopathy. Patient 2 presented with cardiac tamponade, she was later detected to have systemic lupus erythematosus (SLE). Her bone marrow aspirate revealed prominent hemophagocytosis. Both cases improved with pulse methylprednisolone therapy.
引用
收藏
页码：1261 / 1263
页数：2
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