Reactive Hemophagocytic syndrome

被引:0
|
作者
L. Rajam
Vinitha Prasad
B.L. Yatheesha
机构
[1] Amrita Institute of Medical Sciences and Research Center,Department of Pediatrics
[2] Amrita Institute of Medical Sciences and Research Centre,undefined
来源
The Indian Journal of Pediatrics | 2008年 / 75卷
关键词
Reactive hemophagocytic syndrome; Acute lupus hemophagocytic syndrome; Cardiac tamponade;
D O I
暂无
中图分类号
学科分类号
摘要
We describe two cases of Reactive Hemophagocytic syndrome (RHS) occurring in rheumatic diseases in childhood. Patient 1, an adolescent girl with systemic onset Juvenile idopathic arthritis (JRA) presented like severe sepsis with shock, hepatic dysfunction and coagulopathy. Patient 2 presented with cardiac tamponade, she was later detected to have systemic lupus erythematosus (SLE). Her bone marrow aspirate revealed prominent hemophagocytosis. Both cases improved with pulse methylprednisolone therapy.
引用
收藏
页码:1261 / 1263
页数:2
相关论文
共 50 条
  • [1] Reactive Hemophagocytic syndrome
    Rajam, L.
    Prasad, Vinitha
    Yatheesha, B. L.
    INDIAN JOURNAL OF PEDIATRICS, 2008, 75 (12): : 1261 - 1263
  • [2] LIVER CHANGES IN REACTIVE HEMOPHAGOCYTIC SYNDROME
    TSUI, WMS
    WONG, KF
    TSE, CCH
    LIVER, 1992, 12 (06): : 363 - 367
  • [3] REACTIVE HEMOPHAGOCYTIC SYNDROME (RHS) DURING SEPSIS SYNDROME
    STEPHAN, F
    THIOLIERE, B
    COHEN, S
    TULLIEZ, M
    CLERGUE, F
    BRITISH JOURNAL OF ANAESTHESIA, 1994, 72 : 112 - 112
  • [4] REACTIVE HISTIOCYTOSIS, HISTIOCYTOSIS HEMOPHAGOCYTOSIS AND HEMOPHAGOCYTIC SYNDROME
    DIAZ, JDG
    HERRAIZ, CG
    COSTALAGO, MA
    VALES, JMG
    REVISTA CLINICA ESPANOLA, 1990, 186 (04): : 193 - 196
  • [5] Reactive hemophagocytic syndrome: about one case
    Charfeddine, B
    Laradi, S
    Kassab, A
    Ferchichi, S
    El Kissi, M
    Hizem, F
    Baghdadi, S
    Ben Limem, H
    Miled, A
    ANNALES DE BIOLOGIE CLINIQUE, 2003, 61 (01) : 81 - 83
  • [6] Reactive hemophagocytic syndrome and Hodgkin's disease
    Chim, CS
    Hui, PK
    AMERICAN JOURNAL OF HEMATOLOGY, 1997, 55 (01) : 49 - 50
  • [7] Reactive hemophagocytic syndrome: A series of 23 cases
    Tiab, M
    Mechinaud, F
    Hamidou, M
    Gaillard, F
    Raffi, F
    Harousseau, JL
    ANNALES DE MEDECINE INTERNE, 1996, 147 (03): : 138 - 144
  • [8] A Rare Hematological Manifestation of Brucellosis: Reactive Hemophagocytic Syndrome
    Erduran, Erol
    Makuloglu, Melike
    Mutlu, Mehmet
    JOURNAL OF MICROBIOLOGY IMMUNOLOGY AND INFECTION, 2010, 43 (02) : 159 - 162
  • [9] REACTIVE HEMOPHAGOCYTIC SYNDROME - A STUDY OF 7 FATAL CASES
    CHAN, JKC
    NG, CS
    LAW, CK
    NG, WF
    WONG, KF
    PATHOLOGY, 1987, 19 (01) : 43 - 50
  • [10] REACTIVE HEMOPHAGOCYTIC SYNDROME - ANALYSIS OF A SERIES OF 7 CASES
    PECERO, VGR
    MARQUEZ, RL
    LERCHUNDI, MA
    ILLESCAS, MC
    MADRONA, DP
    MEDICINA CLINICA, 1990, 94 (04): : 130 - 134