Erdheim-Chester disease

被引:8
|
作者
Lenahan, SE
Helm, KF
Hopper, KD
机构
[1] Penn State Univ, Milton S Hershey Med Ctr, Dept Dermatol & Pathol, Hershey, PA 17033 USA
[2] Penn State Univ, Milton S Hershey Med Ctr, Dept Pathol, Hershey, PA 17033 USA
[3] Penn State Univ, Milton S Hershey Med Ctr, Dept Radiol, Hershey, PA 17033 USA
关键词
D O I
10.1007/s10227-002-0110-9
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Background: Erdheim-Chester disease is a rare non-Langerhans' cell histiocytosis. Objective: This case report is presented to familiarize clinicians with Erdheim-Chester disease and its differential diagnosis. Results and Conclusion: Erdheim-Chester disease presents with unique clinical and pathologic findings. Its xanthoma-like lesions can cause significant morbidity and mortality.
引用
收藏
页码:129 / 132
页数:4
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