Background: Erdheim-Chester disease is a rare non-Langerhans' cell histiocytosis. Objective: This case report is presented to familiarize clinicians with Erdheim-Chester disease and its differential diagnosis. Results and Conclusion: Erdheim-Chester disease presents with unique clinical and pathologic findings. Its xanthoma-like lesions can cause significant morbidity and mortality.
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Haroche, Julien
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Arnaud, Laurent
Cohen-Aubart, Fleur
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Cohen-Aubart, Fleur
Hervier, Baptiste
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Hervier, Baptiste
Charlotte, Frederic
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Hop La Pitie Salpetriere, AP HP, Dept Anatomopathol, F-75651 Paris 13, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Charlotte, Frederic
Emile, Jean-Francois
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Univ Versailles, Ambroise Pare Hosp, AP HP, Dept Pathol, F-92104 Boulogne, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Emile, Jean-Francois
Amoura, Zahir
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Hop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France
Univ Paris 06, Paris, FranceHop La Pitie Salpetriere, AP HP, Dept Internal Med, French Reference Ctr Rare Autoimmune & Syst Dis, F-75651 Paris 13, France