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- [38] CYSTEAMINE ENHANCES THE PROCOAGULANT ACTIVITY OF FACTOR-VIII-EAST-HARTFORD, A DYSFUNCTIONAL PROTEIN DUE TO A LIGHT CHAIN THROMBIN CLEAVAGE SITE MUTATION (ARGININE-1689 TO CYSTEINE) JOURNAL OF CLINICAL INVESTIGATION, 1992, 89 (05): : 1375 - 1381