ANESTHETIC PROBLEMS IN A CHILD WITH ECTRODACTYLY, ECTODERMAL DYSPLASIA AND CLEFT-LIP PALATE - THE EEC SYNDROME

被引：4
|
作者：
MIZUSHIMA, A
SATOYOSHI, M
机构：
[1] Department of Anesthesiology, Juntendo University School of Medicine, Tokyo, 113, Bunkyo-ku, Hongo
[2] Department of Anesthesiology, Juntendo University School of Medicine, Tokyo, 113, 2-1-1, Hongo, Bunkyo-ku
来源：
ANAESTHESIA | 1992年 / 47卷 / 02期
关键词：
ANESTHESIA; PEDIATRIC; COMPLICATIONS; EEC SYNDROME (ECTRODACTYLY; ECTODERMAL DYSPLASIA; CLEFT LIP AND PALATE); HYPOHIDROSIS;
D O I：
10.1111/j.1365-2044.1992.tb02012.x
中图分类号：
R614 [麻醉学];
学科分类号：
100217 ;
摘要：
The EEC syndrome is a congenital anomaly complex associated with ectrodactyly, ectodermal dysplasia, and cleft lip and palate. We present a patient with the complete form of this syndrome who had undergone eight operations in childhood. The main problems encountered by the anaesthetists were malnutrition, difficulty with control of body temperature related to hypohidrosis and persistent infection of the respiratory tract. Copyright © 1992, Wiley Blackwell. All rights reserved
引用
收藏
页码：137 / 140
页数：4
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