共 50 条
- [42] LYSOSOMAL-ENZYME PRECURSORS IN HUMAN-FIBROBLASTS - ACTIVATION OF CATHEPSIN-D PRECURSOR INVITRO AND ACTIVITY OF BETA-HEXOSAMINIDASE-A PRECURSOR TOWARDS GANGLIOSIDE GM2 EUROPEAN JOURNAL OF BIOCHEMISTRY, 1982, 125 (02): : 317 - 321
- [44] GANGLIOSIDE GM2 LEVELS IN HUMAN-MELANOMA CELLS - INVERSE CORRELATION WITH LYSOSOMAL BETA-HEXOSAMINIDASE-A ACTIVITY BIOCHEMISTRY INTERNATIONAL, 1992, 27 (02): : 343 - 352
- [49] MOLECULAR-BASIS OF ADULT-ONSET AND CHRONIC GM2 GANGLIOSIDOSES IN PATIENTS OF ASHKENAZI JEWISH ORIGIN - SUBSTITUTION OF SERINE FOR GLYCINE AT POSITION 269 OF THE ALPHA-SUBUNIT OF BETA-HEXOSAMINIDASE PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1989, 86 (07) : 2413 - 2417