MAPLE SYRUP URINE DISEASE - ANALYSIS OF BRANCHED-CHAIN KETOACID DECARBOXYLATION IN CULTURED FIBROBLASTS

被引：22

作者：

WENDEL, U ^{[1
]}

WENTRUP, H ^{[1
]}

RUDIGER, HW ^{[1
]}

机构：

[1] UNIV HAMBURG,DEPT HUMAN GENET,DIV CYTOGENET & CLIN GENET,HAMBURG,FED REP GER

来源：

PEDIATRIC RESEARCH | 1975年 / 9卷 / 09期

关键词：

D O I：

10.1203/00006450-197509000-00005

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

引用

页码：709 / 717

页数：9

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