MAPLE SYRUP URINE DISEASE - ANALYSIS OF BRANCHED-CHAIN KETOACID DECARBOXYLATION IN CULTURED FIBROBLASTS

被引:22
|
作者
WENDEL, U [1 ]
WENTRUP, H [1 ]
RUDIGER, HW [1 ]
机构
[1] UNIV HAMBURG,DEPT HUMAN GENET,DIV CYTOGENET & CLIN GENET,HAMBURG,FED REP GER
关键词
D O I
10.1203/00006450-197509000-00005
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
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页码:709 / 717
页数:9
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