Erdheim-Chester disease (ECD) is characterized by lipid granuloma in the long tubular bones, which leads to pathognomonic symmetrical sclerosis of their metaphyses and diaphyses. Lipid granuloma may also be present in numerous other mesenchymal tissues, especially lung, orbit and retroperitoneal space. The clinical course and prognosis of the disease depend on these lesions. Reviewing 30 cases published since 1931 and a personal case with S100 positive cells, we present the typical radiological and clinical findings. There is striking resemblance to chronic disseminated histiocytosis X.
机构:
Casa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, ItalyCasa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, Italy
Gazzeri, R.
Galarza, M.
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Casa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, ItalyCasa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, Italy
Galarza, M.
Amoroso, R.
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Casa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, ItalyCasa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, Italy
Amoroso, R.
De Bonis, C.
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Casa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, ItalyCasa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, Italy
De Bonis, C.
D'Angelo, V.
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Casa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, ItalyCasa Sollievo Sofferenza Hosp, Dept Neurosurg, San Giovanni Rotondo, Italy
D'Angelo, V.
JOURNAL OF NEUROLOGY NEUROSURGERY AND PSYCHIATRY,
2006,
77
(09):
: 1078
-
1078
机构:
Mt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Dickson, Brendan Craig
Pethe, Vaijayanti
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机构:
Mt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Pethe, Vaijayanti
Chung, Catherine Tse-Shing
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机构:
Mt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Chung, Catherine Tse-Shing
Howarth, David John Charles
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机构:
Mt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Howarth, David John Charles
Bilbao, Juan Manuel
论文数: 0引用数: 0
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机构:
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, Canada
Sunnybrook Hlth Sci Ctr, Dept Anat Pathol, Toronto, ON M4N 3M5, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Bilbao, Juan Manuel
Fornasier, Victor Lodovico
论文数: 0引用数: 0
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Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, Canada
St Michaels Hosp, Div Pathol, Toronto, ON M5B 1W8, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Fornasier, Victor Lodovico
Streutker, Catherine Joanne
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机构:
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, Canada
St Michaels Hosp, Div Pathol, Toronto, ON M5B 1W8, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Streutker, Catherine Joanne
Sugar, Linda Marilyn
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机构:
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, Canada
Sunnybrook Hlth Sci Ctr, Dept Anat Pathol, Toronto, ON M4N 3M5, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Sugar, Linda Marilyn
Bapat, Bharati
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Mt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, CanadaMt Sinai Hosp, Samuel Lunenfeld Res Inst, Dept Pathol & Lab Med, Toronto, ON M5T 3L9, Canada
机构:Univ Vita Salute San Raffaele, Unit Med & Clin Immunol, I-20132 Milan, Italy
Cavalli, Giulio
Berti, Alvise
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机构:Univ Vita Salute San Raffaele, Unit Med & Clin Immunol, I-20132 Milan, Italy
Berti, Alvise
Campochiaro, Corrado
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机构:Univ Vita Salute San Raffaele, Unit Med & Clin Immunol, I-20132 Milan, Italy
Campochiaro, Corrado
Dagna, Lorenzo
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机构:
Univ Vita Salute San Raffaele, Unit Med & Clin Immunol, I-20132 Milan, Italy
Ist Sci San Raffaele, I-20132 Milan, ItalyUniv Vita Salute San Raffaele, Unit Med & Clin Immunol, I-20132 Milan, Italy