CONGENITAL AFIBRINOGENEMIA - A CASE-REPORT

被引:11
|
作者
LEENERS, JV [1 ]
MOSSAKOWSKI, J [1 ]
KAYSER, S [1 ]
机构
[1] ELISABETH KINDERKRANKENHAUS,MONCHENGLADBACH RHEYDT,GERMANY
来源
KLINISCHE PADIATRIE | 1995年 / 207卷 / 01期
关键词
D O I
10.1055/s-2008-1046506
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
It is reported about a case of congenital afirinogenaemia on a newborn female. The treatment is described. Congenital afirinogenaemia is a rare autosomal recessiv disorder. There are 250 cases in world literature, mostly with consanguineous parents. Bleeding is usually mild, so that treatment should not be prophylactic, because any blood product might cause complication, like AIDS. Only acute haemorrhage should be treated with fresh frozen plasma or fibrinogen concentrates.
引用
收藏
页码:34 / 35
页数:2
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