CONGENITAL AFIBRINOGENEMIA - A CASE-REPORT

被引：11

作者：

LEENERS, JV ^{[1
]}

MOSSAKOWSKI, J ^{[1
]}

KAYSER, S ^{[1
]}

机构：

[1] ELISABETH KINDERKRANKENHAUS,MONCHENGLADBACH RHEYDT,GERMANY

来源：

KLINISCHE PADIATRIE | 1995年 / 207卷 / 01期

关键词：

D O I：

10.1055/s-2008-1046506

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

It is reported about a case of congenital afirinogenaemia on a newborn female. The treatment is described. Congenital afirinogenaemia is a rare autosomal recessiv disorder. There are 250 cases in world literature, mostly with consanguineous parents. Bleeding is usually mild, so that treatment should not be prophylactic, because any blood product might cause complication, like AIDS. Only acute haemorrhage should be treated with fresh frozen plasma or fibrinogen concentrates.

引用

页码：34 / 35

页数：2

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