LIVER FIBROSIS IN ARGINASE DEFICIENCY

被引:0
|
作者
JORDA, A
PORTOLES, M
RUBIO, V
CAPDEVILA, A
VILAS, J
GARCIAPINO, J
机构
[1] SOCIAL SECUR HOSP JUAN CANALEJO,DEPT PATHOL,LA CORUNA,SPAIN
[2] HOSP MONTECELO,DEPT PEDIAT,PONTEVEDRA,SPAIN
关键词
D O I
暂无
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
引用
收藏
页码:691 / 692
页数:2
相关论文
共 50 条
  • [41] Alcohol Exacerbates Liver Injury and Fibrosis in Mice With Liver-Specific Deficiency of Augmenter of Liver Regeneration
    Kumar, Sudhir
    Dangi, Anil
    Gandhi, Chandrashekhar
    FASEB JOURNAL, 2015, 29
  • [42] Increased arginase activity in cystic fibrosis airways
    Grasemann, H
    Schwiertz, R
    Matthiesen, S
    Racké, K
    Ratjen, F
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2005, 172 (12) : 1523 - 1528
  • [43] Lipid nanoparticle-targeted mRNA therapy as a treatment for the inherited metabolic liver disorder arginase deficiency
    Truong, Brian
    Allegri, Gabriella
    Liu, Xiao-Bo
    Burke, Kristine E.
    Zhu, Xuling
    Cederbaum, Stephen D.
    Haberle, Johannes
    Martini, Paolo G. V.
    Lipshutz, Gerald S.
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2019, 116 (42) : 21150 - 21159
  • [44] ARGINASE DEFICIENCY PRESENTING AS CEREBRAL-PALSY
    SCHEUERLE, AE
    MCVIE, R
    BEAUDET, AL
    SHAPIRA, SK
    PEDIATRICS, 1993, 91 (05) : 995 - 996
  • [45] Anesthesia in a patient with arginase deficiency: implications and management
    Kaul, Naresh
    Khan, Rashid M.
    Sharma, Pradeep K.
    Sumant, Ashok
    PEDIATRIC ANESTHESIA, 2008, 18 (11) : 1139 - 1140
  • [46] Severe infantile presentation of arginase I deficiency
    Ghai, Shailly Jain
    Nagamani, Sandesh C. Sreenath
    Lee, Brendan
    Blaser, Susan
    Feigenbaum, Annette
    MOLECULAR GENETICS AND METABOLISM, 2011, 102 (03) : 291 - 291
  • [47] Human recombinant arginase enzyme reduces plasma arginine in mouse models of arginase deficiency
    Burrage, Lindsay C.
    Sun, Qin
    Elsea, Sarah H.
    Jiang, Ming-Ming
    Nagamani, Sandesh C. S.
    Frankel, Arthur E.
    Stone, Everett
    Alters, Susan E.
    Johnson, Dale E.
    Rowlinson, Scott W.
    Georgiou, George
    Lee, Brendan H.
    HUMAN MOLECULAR GENETICS, 2015, 24 (22) : 6417 - 6427
  • [48] UNSUCCESSFUL TRIAL OF GENE REPLACEMENT IN ARGINASE DEFICIENCY
    TERHEGGEN, HG
    LOWENTHAL, A
    LAVINHA, F
    COLOMBO, JP
    ROGERS, S
    ZEITSCHRIFT FUR KINDERHEILKUNDE, 1975, 119 (01): : 1 - 3
  • [49] Recurrent unexplained hyperammonemia in an adolescent with arginase deficiency
    Zhang, Yan
    Landau, Yuval E.
    Miller, David T.
    Marsden, Deborah
    Berry, Gerard T.
    Kellogg, Mark D.
    CLINICAL BIOCHEMISTRY, 2012, 45 (18) : 1583 - 1586
  • [50] HYPERARGININEMIA WITH RED-CELL ARGINASE DEFICIENCY
    CEDERBAU.SD
    SHAW, KNF
    VALENTE, M
    AMERICAN JOURNAL OF HUMAN GENETICS, 1973, 25 (06) : A20 - A20