AORTIC ATRESIA WITH INTERRUPTION OF THE AORTIC-ARCH AND AN AORTOPULMONARY FISTULOUS TRACT - CASE-REPORT

被引:7
|
作者
DONOFRIO, MT
RAMACIOTTI, C
WEINBERG, PM
MURPHY, JD
机构
[1] Division of Cardiology, The Children's Hospital of Philadelphia, Philadelphia, 19104, PA
关键词
INTERRUPTED AORTIC ARCH; AORTIC ATRESIA; AORTOPULMONARY FISTULOUS TRACT;
D O I
10.1007/BF00801916
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We present a case of interruption of the aortic arch (IAA) in association with aortic atresia. A pulmonary artery to ascending aorta fistulous channel at the level of the sinuses of Valsalva of the pulmonary artery was present and supplied the ascending aorta and coronary arteries. The communication had a significant length, so embryologically it is not an aortopulmonary window. There have been only three reported cases in the literature of IAA with aortic atresia; in none was a pulmonary artery to ascending aorta fistulous tract present.
引用
收藏
页码:147 / 149
页数:3
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