BROWN-VIALETTO-VAN LAERE SYNDROME - REPORT OF 2 CASES

被引：0

作者：

DEOLIVEIRA, JT ^{[1
]}

MOREIRA, PRR ^{[1
]}

CARDOSO, F ^{[1
]}

PERPETUO, FOL ^{[1
]}

机构：

[1] UNIV FED MINAS GERAIS,HOSP CLIN,SERV NEUROL,BELO HORIZONT,MG,BRAZIL

来源：

ARQUIVOS DE NEURO-PSIQUIATRIA | 1995年 / 53卷 / 04期

关键词：

BROWN-VIALETTO-VAN LAERE SYNDROME; PONTOBULBAR PALSY WITH DEAFNESS; MUSCLE SPINAL ATROPHY; HEREDITARY DEAFNESS;

D O I：

暂无

中图分类号：

Q189 [神经科学];

学科分类号：

071006 ;

摘要：

Brown-Vialetto-van Laere syndrome is a rare hereditary or sporadic degenerative disorder characterised by progressive sensoryneural deafness, followed or accompanied by cranial nerve palsies. The anterior horn cells and the optic pathways may be involved in some cases. We report two cases, and comment the differential diagnosis and the relationships of this syndrome to the muscle spinal atrophies and the hereditary deafness.

引用

页码：789 / 791

页数：3

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