A major hallmark of neurofibromatosis type I (NFI) is the development of benign tumors. Hepatoblastomas associated with NFI is reported rarely in the literature. We present here a one year-old girl with both NFI and hepatoblastoma. Hepatoblastoma can be associated with NFI. Abdominal ultrasound is not included within the diagnostic criteria or surveillance of NFI. As NFI can be associated with hepatoblastoma and other abdominal tumors, a careful physical examination and an abdominal USG if necessary should be considered.
机构:
King Abdulaziz Bin Saud Univ, Div Dermatol, Dept Med, King Fahad Natl Guard Hosp, Riyadh 11426, Saudi ArabiaKing Abdulaziz Bin Saud Univ, Div Dermatol, Dept Med, King Fahad Natl Guard Hosp, Riyadh 11426, Saudi Arabia
Bin Amer, Yousef
Al-Khenaizan, Sultan
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King Abdulaziz Bin Saud Univ, Div Dermatol, Dept Med, King Fahad Natl Guard Hosp, Riyadh 11426, Saudi ArabiaKing Abdulaziz Bin Saud Univ, Div Dermatol, Dept Med, King Fahad Natl Guard Hosp, Riyadh 11426, Saudi Arabia
机构:
Univ Turku, Inst Biomed, Dept Cell Biol & Anat, Turku, Finland
Wallac Oy, Med & Sci Affairs, POB 10, Turku 20101, FinlandUniv Turku, Dept Dermatol & Venereol, Turku, Finland
机构:
King Abdulaziz Univ Hosp, Fac Med, Dept Pediat, Jeddah, Saudi ArabiaKing Abdulaziz Univ Hosp, Fac Med, Dept Pediat, Jeddah, Saudi Arabia
Qutub, Lujain
Al-Agha, Abdulmoein
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King Abdulaziz Univ Hosp, Fac Med, Dept Pediat, Jeddah, Saudi Arabia
POB 80215, Jeddah 21589, Saudi ArabiaKing Abdulaziz Univ Hosp, Fac Med, Dept Pediat, Jeddah, Saudi Arabia