EMERGENCY OPERATION FOR THORACIC AORTIC-ANEURYSM CAUSED BY THE EHLERS-DANLOS SYNDROME

被引:10
|
作者
HAMANO, K
MINAMI, Y
FUJIMURA, Y
TSUBOI, H
FURUKAWA, S
ODA, T
ESATO, K
机构
[1] First Department of Surgery, Yamaguchi University School of Medicine, Department of Surgery, Yamaguchi
来源
ANNALS OF THORACIC SURGERY | 1994年 / 58卷 / 04期
关键词
D O I
10.1016/0003-4975(94)90488-X
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Two patients were treated emergently for impending ruptured thoracic aortic aneurysms caused by type IV Ehlers-Danlos syndrome. One patient had typical physical evidence of type IV Ehlers-Danlos syndrome. The other patient had a normal phenotype. Type IV Ehlers-Danlos syndrome was diagnosed by electrophoresis of the collagen extracted from the skin. The clinician must be aware of the variations in presentation of type IV Ehlers-Danlos syndrome.
引用
收藏
页码:1180 / 1182
页数:3
相关论文
共 50 条
  • [31] EHLERS-DANLOS SYNDROME
    BEIGHTON, P
    SOUTH AFRICAN MEDICAL JOURNAL, 1972, 46 (13): : 373 - &
  • [32] Ehlers-Danlos syndrome
    Chen, Chuang-Wei
    Jao, Shu-Wen
    NEW ENGLAND JOURNAL OF MEDICINE, 2007, 357 (11): : E12 - E12
  • [33] EHLERS-DANLOS SYNDROME
    BEIGHTON, P
    ANNALS OF THE RHEUMATIC DISEASES, 1970, 29 (03) : 332 - +
  • [34] THE EHLERS-DANLOS SYNDROME
    HOLT, JF
    AMERICAN JOURNAL OF ROENTGENOLOGY, 1946, 55 (04) : 420 - 426
  • [35] EHLERS-DANLOS SYNDROME
    ZANTKUYL, CF
    DERMATOLOGICA, 1975, 151 (05): : 315 - 315
  • [36] The Ehlers-Danlos Syndrome
    Malfait, Fransiska
    De Paepe, Anne
    PROGRESS IN HERITABLE SOFT CONNECTIVE TISSUE DISEASES, 2014, 802 : 129 - 143
  • [37] Ehlers-Danlos syndrome
    Narayanan, M.
    Watkiss, J.
    ACTA ANAESTHESIOLOGICA SCANDINAVICA, 2009, 53 (07) : 971 - 971
  • [38] The Ehlers-Danlos Syndrome
    Weber, FP
    BRITISH JOURNAL OF DERMATOLOGY AND SYPHILIS, 1936, 48 : 609 - 617
  • [39] EHLERS-DANLOS SYNDROME
    FITCHIE, P
    VETERINARY RECORD, 1972, 90 (06) : 165 - &
  • [40] EHLERS-DANLOS SYNDROME
    CASTILLOFONCERRADA, G
    STANISLAW, S
    PATOLOGIA-MEXICO CITY, 1980, 18 (01): : 80 - 80