A non-BRICHOS surfactant protein c mutation disrupts epithelial cell function and intercellular signaling

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作者
Markus Woischnik
Christiane Sparr
Sunčana Kern
Tobias Thurm
Andreas Hector
Dominik Hartl
Gerhard Liebisch
Surafel Mulugeta
Michael F Beers
Gerd Schmitz
Matthias Griese
机构
[1] Ludwig-Maximilians University,Department of Pneumology, Dr. von Hauner Children's Hospital
[2] University of Regensburg,Institute for Clinical Chemistry and Laboratory Medicine
[3] University of Pennsylvania School of Medicine,Pulmonary and Critical Care Division
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Interstitial Lung Disease; Hydroxychloroquine; Lamellar Body; I73T Mutation; Cytoprotective Mechanism;
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