Delayed Enhancement Cardiac Magnetic Resonance Imaging in Propionic Acidemia

被引:0
|
作者
Satoru Iwashima
Takamichi Ishikawa
Takehiko Ohzeki
Yusaku Endou
机构
[1] Hamamatsu University School of Medicine,Department of Pediatrics
来源
Pediatric Cardiology | 2010年 / 31卷
关键词
Delayed-enhancement cardiac magnetic resonance imaging; Cardiomyopathy in propionic academia; Inborn errors of metabolism;
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学科分类号
摘要
We report on cardiomyopathy in propionic acidemia (PA) diagnosed using delayed-enhancement cardiac magnetic imaging (DECM) in a 27-year-old woman. DECM demonstrated hyperenhancement at the lateral wall of the left ventricle, suggesting myocardial changes occurring after a metabolic crisis, which improved during the convalescent period. DECM was useful for the diagnosis of cardiomyopathy in PA.
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页码:884 / 886
页数:2
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