Delayed-enhancement cardiac magnetic resonance imaging;
Cardiomyopathy in propionic academia;
Inborn errors of metabolism;
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摘要:
We report on cardiomyopathy in propionic acidemia (PA) diagnosed using delayed-enhancement cardiac magnetic imaging (DECM) in a 27-year-old woman. DECM demonstrated hyperenhancement at the lateral wall of the left ventricle, suggesting myocardial changes occurring after a metabolic crisis, which improved during the convalescent period. DECM was useful for the diagnosis of cardiomyopathy in PA.
机构:
Hosp Mae Deus Porto Alegre, Dept Radiol, Porto Alegre, RS, BrazilHosp Mae Deus Porto Alegre, Dept Radiol, Porto Alegre, RS, Brazil
Moraes, Gustavo L.
Higgins, Charles B.
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机构:
Univ Calif San Francisco, Dept Radiol & Biomed Imaging, San Francisco, CA 94143 USAHosp Mae Deus Porto Alegre, Dept Radiol, Porto Alegre, RS, Brazil
Higgins, Charles B.
Ordovas, Karen G.
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h-index: 0
机构:
Univ Calif San Francisco, Dept Radiol & Biomed Imaging, San Francisco, CA 94143 USAHosp Mae Deus Porto Alegre, Dept Radiol, Porto Alegre, RS, Brazil