BIO101 demonstrates combined beneficial effects on muscle and motor neurons in a mouse model of severe spinal muscular atrophy

被引:1
|
作者
Lati, M. [1 ]
Bezier, C. [2 ]
Cottin, S. [2 ]
Lafont, R. [1 ]
Veillet, S. [1 ]
Dilda, P. [1 ]
Charbonnier, F. [2 ]
Biondi, O. [2 ]
机构
[1] Biophytis, Paris, France
[2] Paris Descartes Univ, Paris, France
关键词
D O I
10.1016/j.nmd.2019.06.532
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
P.370
引用
收藏
页码:S189 / S189
页数:1
相关论文
共 50 条
  • [41] Fasudil improves survival and promotes skeletal muscle development in a mouse model of spinal muscular atrophy
    Bowerman, Melissa
    Murray, Lyndsay M.
    Boyer, Justin G.
    Anderson, Carrie L.
    Kothary, Rashmi
    BMC MEDICINE, 2012, 10
  • [42] Aberrant Autophagic Response in The Muscle of A Knock-in Mouse Model of Spinal and Bulbar Muscular Atrophy
    Rusmini, Paola
    Polanco, Maria Josefa
    Cristofani, Riccardo
    Cicardi, Maria Elena
    Meroni, Marco
    Galbiati, Mariarita
    Piccolella, Margherita
    Messi, Elio
    Giorgetti, Elisa
    Lieberman, Andrew P.
    Milioto, Carmelo
    Rocchi, Anna
    Aggarwal, Tanya
    Pennuto, Maria
    Crippa, Valeria
    Poletti, Angelo
    SCIENTIFIC REPORTS, 2015, 5
  • [43] Aberrant Autophagic Response in The Muscle of A Knock-in Mouse Model of Spinal and Bulbar Muscular Atrophy
    Paola Rusmini
    Maria Josefa Polanco
    Riccardo Cristofani
    Maria Elena Cicardi
    Marco Meroni
    Mariarita Galbiati
    Margherita Piccolella
    Elio Messi
    Elisa Giorgetti
    Andrew P. Lieberman
    Carmelo Milioto
    Anna Rocchi
    Tanya Aggarwal
    Maria Pennuto
    Valeria Crippa
    Angelo Poletti
    Scientific Reports, 5
  • [44] Protective effects of butyrate-based compounds on a mouse model for spinal muscular atrophy
    Butchbach, Matthew E. R.
    Lumpkin, Casey J.
    Harris, Ashlee W.
    Saieva, Luciano
    Edwards, Jonathan D.
    Workman, Eileen
    Simard, Louise R.
    Pellizzoni, Livio
    Burghes, Arthur H. M.
    EXPERIMENTAL NEUROLOGY, 2016, 279 : 13 - 26
  • [45] Smn Deficiency Causes Neuritogenesis and Neurogenesis Defects in the Retinal Neurons of a Mouse Model of Spinal Muscular Atrophy
    Liu, Hong
    Beauvais, Ariane
    Baker, Adam N.
    Tsilfidis, Catherine
    Kothary, Rashmi
    DEVELOPMENTAL NEUROBIOLOGY, 2011, 71 (02) : 153 - 169
  • [46] Abolishing Bax-dependent apoptosis shows beneficial effects on spinal muscular atrophy model mice
    Tsai, Ming S.
    Chiu, Yung T.
    Wang, Sue H.
    Hsieh-Li, Hsiu M.
    Lian, Wei C.
    Li, Hung
    MOLECULAR THERAPY, 2006, 13 (06) : 1149 - 1155
  • [47] Synaptic pathology at the neuromuscular junction in a mouse model of childhood motor neuron disease (spinal muscular atrophy)
    Murray, L. M.
    Thomson, D.
    Wishart, T. M.
    Gillingwater, T. H.
    JOURNAL OF ANATOMY, 2008, 212 (01) : 84 - 84
  • [48] In vivo imaging of motor axons and neuromuscular junctions in a mouse model of type III spinal muscular atrophy
    Schaefer, Anneliese M.
    Tenkova, Tanya
    NEUROLOGY, 2007, 68 (12) : A67 - A67
  • [49] Stasimon Contributes to the Loss of Sensory Synapses and Motor Neuron Death in a Mouse Model of Spinal Muscular Atrophy
    Simon, Christian M.
    Van Alstyne, Meaghan
    Lotti, Francesco
    Bianchetti, Elena
    Tisdale, Sarah
    Watterson, D. Martin
    Mentis, George Z.
    Pellizzoni, Livio
    CELL REPORTS, 2019, 29 (12): : 3885 - +
  • [50] Adenoviral-mediated mouse model of motor impairment in distal spinal muscular atrophy type V
    Seo, Ah Jung
    Park, Byung Sun
    Jeong, Na Young
    Kim, Doyen
    Kim, Sunghoon
    Park, Chan
    Jung, Junyang
    Huh, Youngbuhm
    ANIMAL CELLS AND SYSTEMS, 2014, 18 (05) : 311 - 317