MOTOR NEURON DISEASE Progressive muscular atrophy in the ALS spectrum

被引:2
|
作者
Maragakis, Nicholas J. [1 ]
机构
[1] Johns Hopkins Univ Hosp, Dept Neurol, Baltimore, MD 21205 USA
关键词
TESTS;
D O I
10.1038/nrneurol.2010.29
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A large, retrospective analysis of patients with amyotrophic lateral sclerosis (ALS) and progressive muscular atrophy (PMA) indicates that a substantial proportion of PMA patients develop upper motor neuron signs indicative of an ALS diagnosis. The findings suggest that PMA should be considered as part of the ALS spectrum rather than as a distinct entity.
引用
收藏
页码:187 / 188
页数:2
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