A novel mouse model of phospholamban p.Arg14del cardiomyopathy develops heart failure with protein aggregation and is unresponsive to common heart failure drugs

被引:0
|
作者
Eijgenraam, T. R. Tim Ruben [1 ]
Boukens, B. J.
Schouten, E. M. [1 ]
Van De Kolk, C. W. A. [1 ]
Stege, N. M. [1 ]
Van Den Berg, M. P. [1 ]
Van Der Meer, P. [1 ]
Sillje, H. H. W. [1 ]
De Boer, R. A. [1 ]
机构
[1] Univ Med Ctr Groningen, Expt Cardiol, Groningen, Netherlands
关键词
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
P1447
引用
收藏
页码:264 / 264
页数:1
相关论文
共 18 条
  • [11] Antisense Therapy Attenuates Phospholamban p.(Arg14del) Cardiomyopathy in Mice and Reverses Protein Aggregation
    Eijgenraam, Tim R.
    Stege, Nienke M.
    Oliveira Nunes Teixeira, Vivian
    de Brouwer, Remco
    Schouten, Elisabeth M.
    Grote Beverborg, Niels
    Sun, Liu
    Spater, Daniela
    Knoll, Ralph
    Hansson, Kenny M.
    Amilon, Carl
    Janzen, David
    Yeh, Steve T.
    Mullick, Adam E.
    van der Meer, Peter
    de Boer, Rudolf A.
    Sillje, Herman H. W.
    INTERNATIONAL JOURNAL OF MOLECULAR SCIENCES, 2022, 23 (05)
  • [12] Protein Aggregation Is an Early Manifestation of Phospholamban p.(Arg14del)-Related Cardiomyopathy: Development of PLN-R14del-Related Cardiomyopathy
    Eijgenraam, Tim R.
    Boogerd, Cornelis J.
    Stege, Nienke M.
    Teixeira, Vivian Oliveira Nunes
    Dokter, Martin M.
    Schmidt, Lukas E.
    Yin, Xiaoke
    Theofilatos, Konstantinos
    Mayr, Manuel
    van der Meer, Peter
    van Rooij, Eva
    van der Velden, Jolanda
    Sillje, Herman H. W.
    de Boer, Rudolf A.
    CIRCULATION-HEART FAILURE, 2021, 14 (11) : E008532
  • [13] Improving electrocardiogram-based detection of rare genetic heart disease using transfer learning: An application to phospholamban p.Arg14del mutation carriers
    Lopes, Ricardo R.
    Bleijendaal, Hidde
    Ramos, Lucas A.
    Verstraelen, Tom E.
    Amin, Ahmad S.
    Wilde, Arthur A. M.
    Pinto, Yigal M.
    de Mol, Bas A. J. M.
    Marquering, Henk A.
    COMPUTERS IN BIOLOGY AND MEDICINE, 2021, 131 (131)
  • [14] A Heterozygous Phospholamban Variant (p.R14del) Leads to Left Ventricular Involvement and Heart Failure Phenotypes in Arrhythmogenic Right Ventricular Cardiomyopathy
    Han Mo
    Xiumeng Hua
    Mengni Bao
    Zhe Sun
    Xiao Chen
    Mengda Xu
    Jiangping Song
    Phenomics, 2024, 4 : 13 - 23
  • [15] A Heterozygous Phospholamban Variant (p.R14del) Leads to Left Ventricular Involvement and Heart Failure Phenotypes in Arrhythmogenic Right Ventricular Cardiomyopathy
    Mo, Han
    Hua, Xiumeng
    Bao, Mengni
    Sun, Zhe
    Chen, Xiao
    Xu, Mengda
    Song, Jiangping
    PHENOMICS, 2024, 4 (01): : 13 - 23
  • [16] Effects of urocortin II in isolated cardiac myocytes from the muscle LIM protein knockout mouse, a model for dilated cardiomyopathy: Bypass of blunted U-adrenergic response in heart failure
    Dieterle, T
    Belke, DD
    Bale, T
    Vale, WW
    Hoshijima, M
    Chien, KR
    Pfisterer, M
    Buser, P
    Dillmann, WH
    Peterson, KL
    CIRCULATION, 2004, 110 (17) : 604 - 605
  • [17] Ubiquitin-Like Protein ISG15 (Interferon-Stimulated Gene of 15 kDa) in Host Defense Against Heart Failure in a Mouse Model of Virus-Induced Cardiomyopathy
    Rahnefeld, Anna
    Klingel, Karin
    Schuermann, Anett
    Diny, Nicola L.
    Althof, Nadine
    Lindner, Anika
    Bleienheuft, Philipp
    Savvatis, Konstantinos
    Respondek, Dorota
    Opitz, Elisa
    Ketscher, Lars
    Sauter, Martina
    Seifert, Ulrike
    Tschoepe, Carsten
    Poller, Wolfgang
    Knobeloch, Klaus-Peter
    Voigt, Antje
    CIRCULATION, 2014, 130 (18) : 1589 - +
  • [18] Novel, Potent, and Highly Selective Calcium/CalmodulinDependent Protein Kinase II (CaMKII) Inhibitors Reduce Substrate Phosphorylation in Rat Hearts and Prolong Survival in a Mouse Model of Severe Heart Failure
    Takagahara, Shuichi
    Harada, Mioko
    Asada, Mari
    Harada, Masataka
    Hirakata, Masao
    Surks, Howard K.
    Mendelsohn, Michael
    Ikeda, Shota
    CIRCULATION, 2023, 148