Solid pseudopapillary neoplasm of pancreas in a patient of situs inversus totalis

Solid pseudopapillary neoplasm (SPN) in a case of situs inversus totalis (SIT) is a rare occurrence with only one case being reported until now in the literature. SIT presents a technical challenge for the operating surgeon in view of the reversed anatomy hence the operating surgeon should orient himself of the altered anatomy of SIT before contemplating surgery. To the best of our knowledge, spleen-preserving distal pancreatectomy in a patient of SPN with SIT has not been reported until now. We are reporting a case of SPN with SIT who underwent spleen-preserving distal pancreatectomy.