In this study, the language abilities of 30 children with Neurofibromatosis Type 1 (NF1) aged 4-6 years were examined using a standardized measure of language. Relations of language to multiple parental report measures of functional communication, social skills, and attention problems were investigated. Difficulties in core language skills were observed, and more than 1/3 of the children struggled on at least one language index. Language abilities were significantly related to parental report of functional communication, social interaction and communication, and social skills, such that language difficulties may be a risk factor for communication and social interaction challenges and communication-related adaptive behavior in children with NF1. Though receptive language abilities were an area of particular difficulty for many children with NF1, they were not significantly related to parental ratings of social functioning and functional communication. Few significant relations were found between language and parent-reported attention problems, although some trends were noted. Hence attention difficulties in children with NF1 may contribute to, but do not appear to fully account for, language difficulties. In sum, there is an increased risk of language difficulties for young children with NF1, and lab-measured language difficulties appear to relate to everyday communication and social interaction functioning. Published by Elsevier Ltd.
机构:
Childrens Natl Hlth Syst, Ctr Neurosci & Behav Med, Washington, DC USA
George Washington Univ, Sch Med, Dept Pediat, Washington, DC 20052 USA
George Washington Univ, Sch Med, Dept Psychiat, Washington, DC USAMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Walsh, Karin S.
Chisholm, Anita
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Murdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Univ Melbourne, Dept Paediat, Fac Med Dent & Hlth Sci, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Chisholm, Anita
Rouel, Melissa
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Childrens Hosp Westmead, Kids Neurosci Ctr, Westmead, NSW, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Rouel, Melissa
Maier, Alice
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Murdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Maier, Alice
Anderson, Vicki
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Murdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Univ Melbourne, Dept Paediat, Fac Med Dent & Hlth Sci, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Anderson, Vicki
Barton, Belinda
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Childrens Hosp Westmead, Kids Neurosci Ctr, Westmead, NSW, Australia
Univ Sydney, Sch Med, Discipline Child & Adolescent Hlth, Westmead, NSW, Australia
Childrens Hosp Westmead, Childrens Hosp Educ Res Inst, Westmead, NSW, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Barton, Belinda
Silk, Tim
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Deakin Univ, Sch Psychol, Burwood, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Silk, Tim
Korgaonkar, Mayuresh
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Univ Sydney, Brain Dynam Ctr, Westmead Inst Med Res, Westmead, NSW, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Korgaonkar, Mayuresh
Seal, Marc
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Murdoch Childrens Res Inst, Dev Imaging, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Seal, Marc
Lami, Francesca
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Murdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Lami, Francesca
Lorenzo, Jennifer
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Childrens Hosp Westmead, Kids Neurosci Ctr, Westmead, NSW, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Lorenzo, Jennifer
Williams, Katrina
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Monash Univ, Dept Paediat, Clayton, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Williams, Katrina
Dabscheck, Gabriel
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Royal Childrens Hosp Melbourne, Dept Neurol, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Dabscheck, Gabriel
Rae, Caroline D.
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Univ New South Wales, Neurosci Res Australia, Randwick, NSW, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Rae, Caroline D.
Kean, Michael
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机构:
Royal Childrens Hosp Melbourne, Dept Imaging, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Kean, Michael
North, Kathryn N.
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Univ Melbourne, Dept Paediat, Fac Med Dent & Hlth Sci, Parkville, Vic, Australia
Murdoch Childrens Res Inst, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
North, Kathryn N.
Payne, Jonathan M.
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Murdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
Univ Melbourne, Dept Paediat, Fac Med Dent & Hlth Sci, Parkville, Vic, AustraliaMurdoch Childrens Res Inst, Brain & Mind, Parkville, Vic, Australia
机构:
Univ Delaware, Dept Phys Therapy, Newark, DE 19713 USA
Univ Delaware, Biomech & Movement Sci Program, Newark, DE 19713 USA
Univ Delaware, Dept Psychol & Brain Sci, Newark, DE 19713 USAUniv Delaware, Dept Phys Therapy, Newark, DE 19713 USA
Bhat, Anjana N.
Boulton, Aaron J.
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Univ Delaware, Dept Phys Therapy, Newark, DE 19713 USA
Univ Delaware, Dept Psychol & Brain Sci, Newark, DE 19713 USA
Univ Delaware, Ctr Hlth Assessment Res & Translat, Newark, DE 19713 USAUniv Delaware, Dept Phys Therapy, Newark, DE 19713 USA
Boulton, Aaron J.
Tulsky, David S.
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机构:
Univ Delaware, Dept Phys Therapy, Newark, DE 19713 USA
Univ Delaware, Dept Psychol & Brain Sci, Newark, DE 19713 USA
Univ Delaware, Ctr Hlth Assessment Res & Translat, Newark, DE 19713 USAUniv Delaware, Dept Phys Therapy, Newark, DE 19713 USA
机构:
La Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, AustraliaLa Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, Australia
Gilbert, Melissa
Beattie, Erin
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La Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, AustraliaLa Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, Australia
Beattie, Erin
Li, Xia
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机构:
La Trobe Univ, Dept Math & Stat, Melbourne, Vic, AustraliaLa Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, Australia
Li, Xia
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Ridgway, Lael
Lawson, Lauren P.
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La Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, Australia
Univ Queensland, Cooperat Res Ctr Living Autism Autism CRC, Indooroopilly, Qld, AustraliaLa Trobe Univ, Olga Tennison Autism Res Ctr, Sch Psychol & Publ Hlth, Melbourne, Vic, Australia