Primary pulmonary hypertension. A familial form.

被引:0
|
作者
Scherpereel, A [1 ]
Steenhouwer, F [1 ]
Quandalle, P [1 ]
Dennetiere, S [1 ]
Haftel, Y [1 ]
Declercq, N [1 ]
Demarcq, JM [1 ]
机构
[1] CTR HOSP ROUBAIX,SERV SOINS INTENS CARDIOL,ROUBAIX,FRANCE
关键词
primary pulmonary hypertension; familial form; pregnancy;
D O I
暂无
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
The authors present the case of three young female patients, of the same family, with all quickly fatal Primary Pulmonary Hypertension (PPH). Their clinical signs and paraclinical investigations were suggestive of a PPH and excluded all others causes of Pulmonary Hypertension. These observations recall the possible familial cases of this rare and very severe disease. It emphasizes as well the possible revelation of the disease during or after a pregnancy. So the members of this family, essentially first the young women who wish to have children, need a medical detection.
引用
收藏
页码:409 / 412
页数:4
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