On-demand Therapy for Hereditary Angioedema

被引:3
|
作者
Bernstein, Jonathan A. [1 ]
机构
[1] Univ Cincinnati, Allergy Sect, Div Immunol, Dept Internal Med,Coll Med, Cincinnati, OH 45267 USA
关键词
Hereditary angioedema; On-demand therapies; Berinert; Ecallantide; Icatibant; Ruconest; Guidelines; RECOMBINANT HUMAN C1-INHIBITOR; C1 INHIBITOR CONCENTRATE; ACUTE ATTACKS; RECEPTOR ANTAGONIST; CONESTAT ALPHA; MANAGEMENT; ECALLANTIDE; DEFICIENCY; ICATIBANT; EFFICACY;
D O I
10.1016/j.iac.2013.07.004
中图分类号
R392 [医学免疫学];
学科分类号
100102 ;
摘要
Consensus guidelines on hereditary angioedema (HAE) recommend that all patients have access to on-demand treatment of acute attacks. A recent patientcentric guideline recommended that at least 2 on-demand therapies be available because patients often have heterogeneous responses to different medications. Self-administration of therapeutic agents, or administration under supervision by a health care provider in the home setting, is the preferred treatment approach. Future studies are needed to show the benefits of acute on-demand therapies at improving quality of life and reducing morbidity and mortality in patients with HAE.
引用
收藏
页码:487 / +
页数:10
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