The risk for type B aortic dissection in Marfan syndrome

被引:0
|
作者
Setacci, C. [1 ]
Galzerano, G. [1 ]
Setacci, F. [2 ]
Mazzitelli, G. [1 ]
de Donato, G. [1 ]
Ricci, C. [3 ]
机构
[1] Univ Siena, Vasc & Endovasc Surg Unit, Dept Med Surg & Neurol Sci, I-53100 Siena, Italy
[2] Univ Roma La Sapienza, Sch Med, Dept Surg R Valdoni, I-00185 Rome, Italy
[3] Univ Siena, Intervent Radiol Unit, I-53100 Siena, Italy
来源
JOURNAL OF CARDIOVASCULAR SURGERY | 2015年 / 56卷 / 06期
关键词
Collagen diseases; Marfan Syndrome; Connective tissue diseases; INTERNATIONAL REGISTRY; INSIGHTS; MANAGEMENT; MUTATIONS; TGFBR1;
D O I
暂无
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Marfan syndrome is the most prevalent connective tissue disorder, with an autosomal dominant inheritance with variable penetrance. This paper aims to summarize epidemiology and treatment for type B dissection in Marfan patients.
引用
收藏
页码:899 / 904
页数:6
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