Cicatricial pemphigoid (benign mucous membrane pemphigoid)

被引:0
|
作者
Terezhalmy, GT
Bergfeld, WF
机构
[1] Cleveland Clin Fdn, Dept Dent A70, Sect Oral Med, Cleveland, OH 44195 USA
[2] Cleveland Clin Fdn, Dept Anat Pathol, Sect Dermatopathol, Cleveland, OH 44195 USA
来源
QUINTESSENCE INTERNATIONAL | 1998年 / 29卷 / 07期
关键词
D O I
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中图分类号
R78 [口腔科学];
学科分类号
1003 ;
摘要
Cicatricial pemphigoid is a chronic mucocutaneous bullous condition. It is a heterogenous autoimmune disease, characterized by the production of autoantibodies against basement membrane zone antigens. The target antigens in cicatricial pemphigoid appear to be lamina lucida proteins involved in human keratinocyte adhesion to extracellular matrix.(1-3) Cicatricial pemphigoid primarily affects persons older than 40 years and appears to have a 2:1 predilection for women, without racial or geographic bias.
引用
收藏
页码:429 / 434
页数:6
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