German Guideline for Idiopathic Pulmonary Fibrosis

被引：11

作者：

Behr, J. ^{[1
,2
,3
]}

Guenther, A. ^{[3
,4
,5
,6
]}

Bonella, F. ^{[7
]}

Dinkel, J. ^{[3
,8
,9
]}

Fink, L. ^{[10
,11
]}

Geiser, T. ^{[12
]}

Geissler, K. ^{[13
]}

Glaeser, S. ^{[14
,15
]}

Handzhhiev, S. ^{[16
]}

Jonigk, D. ^{[17
,18
]}

Koschel, D. ^{[19
,20
]}

Kreuter, M. ^{[21
,22
]}

Leuschner, G. ^{[1
,2
,3
]}

Markart, P. ^{[4
,23
,24
,25
]}

Prasse, A. ^{[18
,26
,27
]}

Schoenfeld, N. ^{[28
]}

Schupp, J. C. ^{[29
]}

Sitter, H. ^{[30
]}

Mueller-Quernheim, J. ^{[31
]}

Costabel, U. ^{[7
]}

机构：

[1] Klinikum Univ Munchen, Med Klin & Poliklin 5, Munich, Germany

[2] Asklepios Fachkliniken Munchen Gauting, Comprehens Pneumol Ctr, Munich, Germany

[3] Deutsch Zentrums Lungenforsch, Munich, Germany

[4] Univ Klinikum Giessen Marburg, Schwerpunkt Fibrosierende Lungenerkrankungen, Giessen, Germany

[5] Agaples Pneumol Klin Waldhof Elgershausen, Greifenstein, Germany

[6] Univ Giessen, Marburg Lung Ctr, Giessen, Germany

[7] Univ Med Essen, Zentrum Interstitielle & Seltene Lungenkrankheite, Klin Pneumol Ruhrlandklin, Essen, Germany

[8] Klinikum Univ Munchen, LMU, Klin Radiol, Munich, Germany

[9] Asklepios Fachkliniken Munchen, Gauting, Germany

[10] UGP Wetzlar, Inst Pathol & Zytol, Wetzlar, Germany

[11] Deutsch Zentrums Lungenforsch, Wetzlar, Germany

[12] Univ Bern, Univ Spital, Univ Klin Pneumol, Bern, Switzerland

[13] Patientenvertretung Lungenfibrose eV, Essen, Germany

[14] Vivantes Klinikum Neukolln & Spandau Berlin, Klin Innere Med Pneumol & Infektiol, Berlin, Germany

[15] Univ Med Greifswald, Greifswald, Germany

[16] Univ Klinikum Krems, Klin Abt Pneumol, Krems An Der Donau, Austria

[17] Hannover Med Sch, Inst Pathol, Hannover, Germany

[18] Deutsch Zentrums Lungenforsch, Hannover, Germany

[19] Univ Klinikum Carl Gustav Carus, Abt Innere Med Pneumol, Fachkrankenhaus Coswig, Zentrum Pneumol Allergol Beatmungsmed Thoraxchiru, Dresden, Germany

[20] Univ Klinikum Carl Gustav Carus, Med Klin 1, Bereich Pneumol, Dresden, Germany

[21] Univ Klinikum Heidelberg, Zentrum Interstitielle & Seltene Lungenerkrankung, Thoraxklin, Heidelberg, Germany

[22] Deutsch Zentrums Lungenforsch, Heidelberg, Germany

[23] Justus Liebig Univ Giessen, Univ Giessen Marburg Lung Ctr, Giessen, Germany

[24] Univ Med Marburg, Med Klin 5, Campus Fulda, Fulda, Germany

[25] Deutsch Zentrums Lungenforsch, Fulda, Germany

[26] Hannover Med Sch, Klin Pneumol, Hannover, Germany

[27] Fraunhofer Inst ITEM, Clin Res Ctr, Hannover, Germany

[28] Helios Klinikum Emilvon Behring, Klin Pneumol, Lungenklin Heckeshorn, Berlin, Germany

[29] Yale Univ, Pulm Crit Care & Sleep Med, Yale Sch Med, New Haven, CT USA

[30] Arbeitsgemeinschaft Wissenschaftlichen Med Fachge, Berlin, Germany

[31] Albert Ludwigs Univ, Dept Innere Med, Med Fak, Klin Pneumol, Freiburg, Germany

来源：

PNEUMOLOGIE | 2020年 / 74卷 / 05期

关键词：

INTERSTITIAL LUNG-DISEASE; RESOLUTION COMPUTED-TOMOGRAPHY; VIDEO-ASSISTED THORACOSCOPY; TRANSBRONCHIAL CRYOBIOPSY; BRONCHOALVEOLAR LAVAGE; ACUTE EXACERBATION; FLEISCHNER-SOCIETY; DIAGNOSTIC YIELD; SURGICAL BIOPSY; OCCUPATIONAL-EXPOSURE;

D O I：

10.1055/a-1120-3531

中图分类号：

R56 [呼吸系及胸部疾病];

学科分类号：

摘要：

Idiopathic pulmonary fibrosis (IPF) is a severe and often fatal disease. Diagnosis of IPF requires considerable expertise and experience. Since publication of the international IPF guideline in the year 2011 and Update 2018 several studies and technical advances occurred, which made a new assessment of the diagnostic process mandatory. In view of the antifibrotic drugs which have been approved for the treatment of IPF patients, the goal of this guideline is to foster early, confident and effective diagnosis of IPF. The guideline focusses on the typical clinical setting of an IPF patient and provides tools to exclude known causes of interstitial lung disease including standardised questionnaires, serologic testing and cellular analysis of bronchoalveolar lavage. High resolution computed tomography remains crucial in the diagnostic work-up. If it is necessary to obtain specimen for histology transbronchial lung cryobiopsy is the primary approach, while surgical lung biopsy is reserved for patients who are fit for it and in whom bronchoscopic diagnosis did not provide the information needed. Despite considerable progress, IPF remains a diagnosis of exclusion and multidisciplinary discussion remains the golden standard of diagnosis.

引用

页码：263 / 293

页数：31

共 50 条

[21] Idiopathic pulmonary fibrosis
Harari, S
Caminati, A
ALLERGY, 2005, 60 (04) : 421 - 435
[22] Idiopathic Pulmonary Fibrosis
Prasse, A.
PNEUMOLOGIE, 2015, 69 (10): : 608 - 614
[23] IDIOPATHIC PULMONARY FIBROSIS
PARIENTE, R
GAZETTE MEDICALE, 1985, 92 (03): : 51 - &
[24] IDIOPATHIC PULMONARY FIBROSIS
SELMAN, M
REVISTA MEDICA DE CHILE, 1985, 113 (03) : 260 - 263
[25] Idiopathic pulmonary fibrosis
Maitre, B
REVUE DES MALADIES RESPIRATOIRES, 2001, 18 (06) : S39 - S41
[26] Idiopathic pulmonary fibrosis
Benegas Urteaga, M.
Ramirez Ruz, J.
Sanchez Gonzalez, M.
RADIOLOGIA, 2022, 64 : 227 - 239
[27] Idiopathic pulmonary fibrosis
Xaubet, Antoni
Ancochea, Julio
Molina-Molina, Maria
MEDICINA CLINICA, 2017, 148 (04): : 170 - 175
[28] IDIOPATHIC PULMONARY FIBROSIS
MORGAN, JE
BARKMAN, HW
WARING, NP
SEMINARS IN RESPIRATORY MEDICINE, 1984, 5 (03): : 255 - 263
[29] Idiopathic pulmonary fibrosis
Cottin, Vincent
Cordier, Jean-Francois
PRESSE MEDICALE, 2008, 37 (11): : 1581 - 1590
[30] Idiopathic pulmonary fibrosis
Bewig, B.
PNEUMOLOGE, 2005, 2 (06): : 457 - 467

← 1 2 3 4 5 →