A large sellar granular cell tumor in a 21-year-old woman

被引:20
|
作者
Popovic, Vera
Pekic, Sandra
Skender-Gazibara, Milica
Salehi, Fateme
Kovacs, Kalman
机构
[1] Univ Clin Ctr, Inst Endocrinol, Neuroendocrine Unit, Belgrade 11000, Serbia
[2] Univ Clin Ctr, Fac Med, Inst Pathol, Belgrade 11000, Serbia
[3] Univ Toronto, St Michaels Hosp, Dept Lab Med, Toronto, ON M5B 1W8, Canada
关键词
granular cell tumor; hypopituitarism; pathology;
D O I
10.1007/s12022-007-0013-9
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We report here the case of a 21-year-old woman with a large sellar tumor, extending to the suprasellar area associated with growth hormone deficiency, hypogonadism, hypocorticism, and hyperprolactinemia. Transsphenoidal surgery was performed, and histologic, immunohistochemical, and electron microscopic study lead to the diagnosis of granular cell tumor. These tumors are, in most cases, very small and are found incidentally at autopsy of older patients. Our case is exceptional because the tumor developed in a young woman, extended to the suprasellar region, and caused clinical symptoms.
引用
收藏
页码:91 / 94
页数:4
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