THE PROCESSING AND FUNCTION OF FERRET WILD TYPE AND ΔF508 CFTR

被引：0
|
作者：
Fisher, J. T. [1 ]
Liu, X. [1 ]
Luo, M.
Lukacs, G. [2 ]
Engelhardt, J. F. [1 ]
机构：
[1] Univ Iowa, Ctr Gene Therapy, Iowa City, IA USA
[2] McGill Univ, Montreal, PQ, Canada
来源：
PEDIATRIC PULMONOLOGY | 2010年
关键词：
D O I：
暂无
中图分类号：
R72 [儿科学];
学科分类号：
100202 ;
摘要：
引用
收藏
页码：233 / 234
页数：2
相关论文
共 50 条
  • [41] 4-Chlorobenzo[F]isoquinoline (CBIQ), a novel activator of CFTR and ΔF508 CFTR
    Murthy, M
    Pedemonte, N
    MacVinish, L
    Galietta, L
    Cuthbert, A
    EUROPEAN JOURNAL OF PHARMACOLOGY, 2005, 516 (02) : 118 - 124
  • [42] NOVEL SMALL MOLECULE CORRECTORS AND POTENTIATORS OF ΔF508 CFTR
    Pregel, M.
    DeVit, M.
    Fleming, J.
    Elbaum, D.
    Balch, W.
    Pedemonte, N.
    Galietta, L. J.
    Rutkowski, J.
    Weigel, C.
    DesRosiers, R.
    Liang, F.
    Eskin, J.
    Li, C.
    Bulawa, C.
    Labaudiniere, R.
    PEDIATRIC PULMONOLOGY, 2009, : 287 - 288
  • [43] MOLECULAR BASIS FOR THE TRIAGE DECISION FOR DEGRADATION OF ΔF508 CFTR
    Chio, C. M.
    Agard, D. A.
    PEDIATRIC PULMONOLOGY, 2020, 55 : S72 - S72
  • [44] MECHANISMS FOR RESCUE OF CORRECTABLE FOLDING DEFECTS IN CFTRΔF508
    Grove, D.
    Rosser, M. F.
    Ren, H.
    Cyr, D. M.
    PEDIATRIC PULMONOLOGY, 2009, : 229 - 229
  • [45] ΔF508 mutation increases conformational flexibility of CFTR protein
    Wieczorek, G.
    Zielenkiewcz, P.
    JOURNAL OF CYSTIC FIBROSIS, 2008, 7 (04) : 295 - 300
  • [46] Mechanisms for Rescue of Correctable Folding Defects in CFTRΔF508
    Grove, Diane E.
    Rosser, Meredith F. N.
    Ren, Hong Yu
    Naren, Anjaparavanda P.
    Cyr, Douglas M.
    MOLECULAR BIOLOGY OF THE CELL, 2009, 20 (18) : 4059 - 4069
  • [47] Defective phosphorylation activation of the Delta F508 CFTR.
    Hwang, TC
    AlNakkash, L
    BIOPHYSICAL JOURNAL, 1997, 72 (02) : TUAM7 - TUAM7
  • [48] TNFα EFFECT ON MATURATION OF CFTR DURING INFLAMMATION IN ΔF508 CFTR AND CFTR EXPRESSING CELLS
    Bitam, S.
    Pranke, I
    Tondelier, D.
    Hatton, A.
    Moriceau, S.
    Moquereau, C.
    Sermet-Gaudelus, I
    Ollero, M.
    Edelman, A.
    PEDIATRIC PULMONOLOGY, 2013, 48 : 224 - 225
  • [49] Pharmacological modulation of ion transport across wild-type and ΔF508 CFTR-expressing human bronchial epithelia
    Devor, DC
    Bridges, RJ
    Pilewski, JM
    AMERICAN JOURNAL OF PHYSIOLOGY-CELL PHYSIOLOGY, 2000, 279 (02): : C461 - C479
  • [50] CFTR: folding, misfolding and correcting the ΔF508 conformational defect
    Lukacs, Gergely L.
    Verkman, A. S.
    TRENDS IN MOLECULAR MEDICINE, 2012, 18 (02) : 81 - 91
12345