[1] Univ Milan, Dept Pathophysiol & Transplantat, Milan, Italy
[2] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Dept Internal Med, Resp Unit, Milan, Italy
[3] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Cyst Fibrosis Adult Ctr, Milan, Italy
[4] Univ Sassari, Dept Clin & Expt Med, Clin Epidemiol & Med Stat Unit, Sassari, Italy
[5] Fdn IRCCS Ca Granda Osped Maggiore Policlin, Med Genet Lab, Milan, Italy
[6] AOVR, Verona Cyst Fibrosis Ctr, Verona, Italy