Overlapping polyclonal lymphoproliferative disorders

被引:0
|
作者
Bonometti, Ramona [1 ]
Bellan, Mattia [4 ]
Sola, Daniele [1 ]
Gibbin, Antonello [1 ]
Gavelli, Francesco [2 ]
Patrucco, Filippo [2 ]
Spina, Paolo [3 ]
Gualerzi, Alessandro [1 ]
Favretto, Serena [1 ]
Castello, Luigi Mario [2 ]
Sainaghi, Pier Paolo [4 ]
Pirisi, Mario [4 ]
机构
[1] AOU Maggiore della Carita, Div Internal Med, Novara, Italy
[2] Univ Piemonte Orientale UPO, Dept Translat Med, Novara, Italy
[3] Univ Piemonte Orientale UPO, Dept Pathol, Novara, Italy
[4] Interdisciplinary Res Ctr Autoimmune Dis, IRCAD, Novara, Italy
来源
NATIONAL MEDICAL JOURNAL OF INDIA | 2020年 / 33卷 / 06期
关键词
IGG4-RELATED DISEASE; POEMS SYNDROME; DIAGNOSIS;
D O I
10.4103/0970-258X.321144
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Multicentric Castleman disease (MCD) is a rare clinical entity characterized by a polyclonal lymphoid proliferation, leading to generalized lymphadenopathy, organomegaly and systemic symptoms. It has been reported in association with either other monoclonal or polyclonal lymphoid disorders, such as POEMS syndrome and immunoglobulin (Ig)G4-related disease. We present a patient showing a variant of MCD, sharing common features with POEMS syndrome and associated with the proliferation of IgG4-producing plasma cells.
引用
收藏
页码:344 / 346
页数:3
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