Primary presentation of sarcoidosis with profound bilateral sensorineural hearing loss

被引:0
|
作者
Pandey, Gargi [1 ]
McClenaghan, Fiona [1 ]
Nash, Robert [1 ]
机构
[1] Great Ormond St Hosp Sick Children, Ear Nose & Throat Surg Dept, London, England
关键词
ear; nose and throat; otolaryngology; general practice; family medicine; neuro-otology;
D O I
10.1136/bcr-2021-244140
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
We present a case of a 7-year-old Afro-Caribbean girl presenting with rapidly progressive bilateral sensorineural hearing loss. She was found to have an elevated Angiotensin converting enzyme (ACE) and mediastinal lymphadenopathy containing non-caseating granulomas with multinucleate giant cells, in keeping with sarcoidosis. Cranial imaging demonstrated labyrinthitis. She underwent urgent bilateral cochlear implantation with rehabilitation of hearing sufficient to restart education within 1 month.
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页数:3
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