A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle

被引:0
|
作者
Raso, Irene [1 ]
Quarti, Andrea [2 ]
Chessa, Massimo [3 ]
Basile, Domenica Paola [3 ]
Saracino, Antonio [3 ]
D'Aiello, Angelo Fabio [3 ]
Raineri, Claudia [1 ]
Carminati, Mario [3 ]
Giamberti, Alessandro [4 ]
机构
[1] Univ Pavia, Dept Cardiol, Fdn IRCCS Policlin San Matteo, Pavia, Italy
[2] Azienda Osped Univ Bologna, Dept Congenital Cardiac Surg, Policlin St Orsola Malpighi, Bologna, Italy
[3] IRCCS Policlin San Donato, Pediat & Adult Congenital Heart Ctr, San Donato Milanese, Italy
[4] IRCCS Policlin San Donato, Congenital Cardiac Surg Ctr, San Donato Milanese, Italy
关键词
D O I
10.1177/2150135119894292
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.
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页码:358 / 360
页数:3
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