A Misdiagnosed Case of Double Outlet Right Atrium Associated With Hypoplastic Right Ventricle

被引：0

作者：

Raso, Irene ^{[1
]}

Quarti, Andrea ^{[2
]}

Chessa, Massimo ^{[3
]}

Basile, Domenica Paola ^{[3
]}

Saracino, Antonio ^{[3
]}

D'Aiello, Angelo Fabio ^{[3
]}

Raineri, Claudia ^{[1
]}

Carminati, Mario ^{[3
]}

Giamberti, Alessandro ^{[4
]}

机构：

[1] Univ Pavia, Dept Cardiol, Fdn IRCCS Policlin San Matteo, Pavia, Italy

[2] Azienda Osped Univ Bologna, Dept Congenital Cardiac Surg, Policlin St Orsola Malpighi, Bologna, Italy

[3] IRCCS Policlin San Donato, Pediat & Adult Congenital Heart Ctr, San Donato Milanese, Italy

[4] IRCCS Policlin San Donato, Congenital Cardiac Surg Ctr, San Donato Milanese, Italy

来源：

WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY | 2020年 / 11卷 / 03期

关键词：

D O I：

10.1177/2150135119894292

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Double outlet right atrium (DORA) is a rare congenital heart disease in which the right atrium opens into both ventricles. The reduced leftward motion of the interventricular septum causes a malalignment between the atrial and the ventricular septum at the cardiac crux, which is the pathognomonic feature of this heart defect. We describe a case of significant exertional desaturation in an adult patient who was diagnosed with DORA, restrictive right ventricle, and anomalous tricuspid valve. Subsequently, the patient underwent one-and-a-half ventricular palliation.

引用

页码：358 / 360

页数：3

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