The challenges of closing an ileostomy in patients with total intestinal aganglionosis after small bowel transplant

被引：2

作者：

Jazi, Fereshteh Salimi ^{[1
]}

Sinclair, Tiffany J. ^{[2
]}

Thorson, Chad M. ^{[1
]}

Castillo, Ricardo ^{[3
]}

Bonham, Andrew C. ^{[4
]}

Esquivel, Carlos O. ^{[4
]}

Bruzoni, Matias ^{[1
]}

机构：

[1] Stanford Univ, Lucile Packard Childrens, Div Pediat Surg, Dept Surg,Sch Med, 300 Pasteur Dr,Alway Bldg M116,MC 5733, Stanford, CA 94305 USA

[2] Stanford Univ, Dept Surg, Sch Med, 300 Pasteur Dr Rm H3691, Stanford, CA 94306 USA

[3] Stanford Univ, Div Gastroenterol, Lucile Packard Childrens, Sch Med, 300 Pasteur Dr,Alway Bldg M116,MC 5733, Stanford, CA 94305 USA

[4] Stanford Univ, Div Transplant Surg, Sch Med, 300 Pasteur Dr Rm H3691, Stanford, CA 94306 USA

来源：

PEDIATRIC SURGERY INTERNATIONAL | 2018年 / 34卷 / 01期

关键词：

Total intestinal aganglionosis; Small bowel transplantation; Hirschsprung's disease; TOTAL COLONIC AGANGLIONOSIS; HIRSCHSPRUNG DISEASE; PULL-THROUGH; EXPERIENCE; OUTCOMES; INVOLVEMENT; MANAGEMENT; CHILDREN;

D O I：

10.1007/s00383-017-4216-y

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

We present the case of a 14-year-old male with a history of small bowel transplantation for long segment Hirschsprung's disease who underwent Duhamel ileorectal pull-through procedure. In post-transplant, the patient had no restrictions and was not TPN-dependent. To improve his quality of life, he and his family were interested in closing the ileostomy and undergoing pull-through surgery. The complexity of the case includes the presence of an aganglionic rectal segment-a short root of the mesentery due to the small bowel transplant-and significant immunosuppression. At the moment, he is continent, doing well, and has not had any remarkable complications.

引用

页码：113 / 116

页数：4

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