Lung disease in cystic fibrosis: is airway surface liquid composition abnormal?

被引：30
|
作者：
Verkman, AS
机构：
[1] Univ Calif San Francisco, Cardiovasc Res Inst, Dept Med, San Francisco, CA 94143 USA
[2] Univ Calif San Francisco, Cardiovasc Res Inst, Dept Physiol, San Francisco, CA 94143 USA
来源：
AMERICAN JOURNAL OF PHYSIOLOGY-LUNG CELLULAR AND MOLECULAR PHYSIOLOGY | 2001年 / 281卷 / 02期
关键词：
D O I：
10.1152/ajplung.2001.281.2.L306
中图分类号：
Q4 [生理学];
学科分类号：
071003 ;
摘要：
引用
收藏
页码：L306 / L308
页数：3
相关论文
共 50 条
  • [31] Microbiology of Cystic Fibrosis Airway Disease
    Blanchard, Ana C.
    Waters, Valerie J.
    SEMINARS IN RESPIRATORY AND CRITICAL CARE MEDICINE, 2019, 40 (06) : 727 - 736
  • [32] Abnormal surface liquid pH regulation by cultured cystic fibrosis bronchial epithelium
    Coakley, RD
    Grubb, BR
    Paradiso, AM
    Gatzy, JT
    Johnson, LG
    Kreda, SM
    O'Neal, WK
    Boucher, RC
    PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 2003, 100 (26) : 16083 - 16088
  • [33] Airway inflammation and lung function in cystic fibrosis
    Wainwright, Claire E.
    RESPIROLOGY, 2023, 28 (06) : 509 - 510
  • [34] Prostasin expression is regulated by airway surface liquid volume and is increased in cystic fibrosis
    Myerburg, M. M.
    McKenna, E. E.
    Frizzell, R.
    Luke, C. J.
    Kleyman, T. R.
    Pilewski, J. M.
    PEDIATRIC PULMONOLOGY, 2007, : 235 - 235
  • [35] REDUCED PH AND ELEVATED VISCOSITY OF PORCINE CYSTIC FIBROSIS AIRWAY SURFACE LIQUID
    Tang, X.
    Moninger, T. O.
    Welsh, M. J.
    PEDIATRIC PULMONOLOGY, 2011, : 236 - 236
  • [36] Blocking Airway Surface Liquid Acidification Increases Bacterial Killing In Cystic Fibrosis
    Shah, V. S.
    Ernst, S. E.
    Launspach, J. L.
    Ostedgaard, L.
    Randak, C. O.
    Welsh, M.
    AMERICAN JOURNAL OF RESPIRATORY AND CRITICAL CARE MEDICINE, 2015, 191
  • [37] Proteome of airway surface liquid and mucus in newborn wildtype and cystic fibrosis piglets
    Ana M. Rodriguez-Piñeiro
    Florian Jaudas
    Nikolai Klymiuk
    Andrea Bähr
    Gunnar C. Hansson
    Anna Ermund
    Respiratory Research, 24
  • [38] REDUCED PH INCREASES VISCOSITY OF PORCINE CYSTIC FIBROSIS AIRWAY SURFACE LIQUID
    Tang, X.
    Moninger, T. O.
    Stoltz, D. A.
    Welsh, M. J.
    PEDIATRIC PULMONOLOGY, 2013, 48 : 240 - 240
  • [39] Proteome of airway surface liquid and mucus in newborn wildtype and cystic fibrosis piglets
    Rodriguez-Pineiro, Ana M.
    Jaudas, Florian
    Klymiuk, Nikolai
    Baehr, Andrea
    Hansson, Gunnar C.
    Ermund, Anna
    RESPIRATORY RESEARCH, 2023, 24 (01)
  • [40] Airway surface liquid acidification initiates host defense abnormalities in Cystic Fibrosis
    Juliette Simonin
    Emmanuelle Bille
    Gilles Crambert
    Sabrina Noel
    Elise Dreano
    Aurélie Edwards
    Aurélie Hatton
    Iwona Pranke
    Bérengère Villeret
    Charles-Henry Cottart
    Jean-Patrick Vrel
    Valérie Urbach
    Nesrine Baatallah
    Alexandre Hinzpeter
    Anita Golec
    Lhousseine Touqui
    Xavier Nassif
    Luis J. V Galietta
    Gabrielle Planelles
    Jean-Michel Sallenave
    Aleksander Edelman
    Isabelle Sermet-Gaudelus
    Scientific Reports, 9
12345