Haemorheological profile in congenital afibrinogenemia and in congenital dysfibrinogenemia: A clinical case report

被引：4
|
作者：
Caimi, G. [1 ]
Raso, S. [1 ]
Napolitano, M. [1 ]
Hopps, E. [1 ]
Lo Presti, R. [2 ]
Siragusa, S. [1 ]
机构：
[1] Univ Palermo, Dept Hlth Promot Mother & Child Care, Internal Med & Med Specialties, Via Vespro 129, I-90127 Palermo, Italy
[2] Univ Palermo, Dept Psychol Educ Sci & Human Movement, Palermo, Italy
来源：
CLINICAL HEMORHEOLOGY AND MICROCIRCULATION | 2019年 / 73卷 / 04期
关键词：
BLOOD-CELL AGGREGATION; ACQUIRED DYSFIBRINOGENEMIA; SIALIC-ACID; THROMBOEMBOLIC EVENTS; PLASMA VISCOSITY; FIBRINOGEN; FEATURES; MECHANISMS; THROMBOSIS; PATIENT;
D O I：
10.3233/CH-180542
中图分类号：
R5 [内科学];
学科分类号：
1002 ; 100201 ;
摘要：
Although the inherited quantitative and qualitative disorders of fibrinogen are rare, in the course of time patients may develop complications including episodes of arterial and venous thrombosis. It can be useful to complete the laboratory assessment of these clinical conditions with the evaluation of the haemorheological profile. The data obtained from this study showed that congenital afibrinogenemia was characterized by a primary plasma hypoviscosity, whereas congenital dysfibrinogenemia by a primary plasma hyperviscosity. Both these haemorheological alterations may concur, with different mechanisms, to the pathogenesis of thrombotic vascular complications.
引用
收藏
页码：523 / 530
页数：8
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