Inherited platelet disorders are important causes of bleeding that can quantitatively and qualitatively alter platelets, impairing their function. The purpose of this review is to summarize current knowledge on the different types of inherited platelet disorders, their clinical and laboratory features, molecular genetic causes, and the therapies used in clinical practice to manage these conditions. (C) 2003 Lippincott Williams Wilkins.
机构:
Hosp Sick Children, Res Inst, Div Haematol Oncol, Translat Med, Toronto, ON, Canada
Univ Toronto, Dept Lab Med & Pathobiol, Toronto, ON, Canada
Univ Toronto, Dept Biochem, Toronto, ON, Canada
Univ Toronto, Dept Paediat, Toronto, ON, CanadaHosp Sick Children, Res Inst, Div Haematol Oncol, Translat Med, Toronto, ON, Canada
Rand, Margaret L.
Reddy, Emily C.
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机构:
Hosp Sick Children, Res Inst, Dev & Stem Cell Biol, Toronto, ON, CanadaHosp Sick Children, Res Inst, Div Haematol Oncol, Translat Med, Toronto, ON, Canada
Reddy, Emily C.
Israels, Sara J.
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CancerCare Manitoba, Res Inst Oncol & Hematol, Winnipeg, MB, Canada
Univ Manitoba, Dept Pediat & Child Hlth, Winnipeg, MB, CanadaHosp Sick Children, Res Inst, Div Haematol Oncol, Translat Med, Toronto, ON, Canada