Pyloric Atresia Associated with Epidermolysis Bullosa

被引：0

作者：

Sahebpor, Alireza Alam ^{[1
]}

Ghafari, Vajihe ^{[1
]}

Shokohi, Leila ^{[1
]}

机构：

[1] Mazandaran Univ Med Sci, Dept Pediat Surg, Sari, Iran

来源：

INDIAN PEDIATRICS | 2008年 / 45卷 / 10期

关键词：

Epidermolysis bullosa; Pyloric atresia; Surgery; Survival;

D O I：

暂无

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

We present 5 cases of pyloric atresia associated with junctional epidermolysis bullosa, from 2003 to 2005. Patients underwent laparatomy after stabilization. Four neonates had gastroduodenostomy, and the other had excision of membrane and pyloroplasty. Four survived and one died from fulminant septicemia. Although the association of pyloric atresia with epidermolysis bullosa has been reported to be fatal, our study showed good survival rate.

引用

页码：849 / 851

页数：3

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