Coarctation of the Aorta: Diagnosis and Management

被引:14
|
作者
Raza, Sadaf [1 ]
Aggarwal, Suneil [1 ]
Jenkins, Petra [1 ]
Kharabish, Ahmed [2 ,3 ]
Anwer, Shehab [4 ]
Cullington, Damien [1 ]
Jones, Julia [1 ]
Dua, Jaspal [1 ]
Papaioannou, Vasileios [1 ]
Ashrafi, Reza [1 ]
Moharem-Elgamal, Sarah [1 ,5 ]
机构
[1] Liverpool Heart & Chest Hosp, Adult Congenital Heart Dis Ctr, Liverpool L14 3PE, England
[2] Liverpool Heart & Chest Hosp, Radiol Dept, Liverpool L14 3PE, England
[3] Al Kasr Al Aini, Radiol Dept, Cairo 11562, Egypt
[4] Univ Zurich, Cardiol Dept, CH-8006 Zurich, Switzerland
[5] Natl Heart Inst, Cardiol Dept, Giza 11111, Egypt
关键词
coarctation of the aorta; congenital heart disease; diagnostic imaging; intervention; surgery; CONGENITAL HEART-DISEASE; SMOOTH-MUSCLE-CELLS; SUCCESSFUL REPAIR; FOLLOW-UP; PRENATAL-DIAGNOSIS; ADULT PATIENTS; NEURAL CREST; ARCH SHAPE; PREGNANCY; STENT;
D O I
10.3390/diagnostics13132189
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Coarctation of the aorta (CoA) accounts for approximately 5-8% of all congenital heart defects. Depending on the severity of the CoA and the presence of associated cardiac lesions, the clinical presentation and age vary. Developments in diagnosis and management have improved outcomes in this patient population. Even after timely repair, it is important to regularly screen for hypertension. Patients with CoA require lifelong follow-up with a congenital heart disease specialist as these patients may develop recoarctation and complications at the repair site and remain at enhanced cardiovascular risk throughout their lifetime.
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页数:18
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