Arrhythmogenic Cardiomyopathy Evolving Diagnostic Criteria and Insight from Cardiac Magnetic Resonance Imaging

ACM is a term that encompasses a wide variety of heterogeneous hereditary and nonhereditary dis-orders that can result in cardiac arrhythmias. Although the arrhythmic components of these conditions overlap, they vary greatly in clinical course and therapeutic approach. Over the past few decades, significant strides have been made to better understand the underly-ing pathophysiology and disease process for these conditions enabling individualized patient -centric diagnosis and management approach. The role of CMR is of paramount importance, as it plays an essential role in accurate initial diag-nosis (Fig. 12) and assists in clinical decision -making and follow-up for affected individuals and families. Although the role of CMR has been high-lighted in recent diagnostic criteria, it remains markedly underutilized. Future research is needed to assess the value of advanced tissue characterization techniques in identifying patients with early subclinical pheno-types. There is also aspiration that MRI-driven data will be incorporated in future risk calculators for pre-diction of arrhythmias and guidance of therapy.