Purpose of reviewThis review synthesizes the expanding evidence for pulmonary rehabilitation that has led to its recommended inclusion in the holistic care of people with idiopathic pulmonary fibrosis (IPF), as well as discussing strategies that may maximize and sustain benefits.Recent findingsPulmonary rehabilitation is an effective intervention leading to significant improvements in exercise tolerance, symptoms, and quality of life for people with IPF. Improvements in symptoms and quality of life can persist longer term, whereas functional capacity does not; therefore, strategies to preserve functional capacity are an important area of research. Referral early in the disease course is encouraged to promote longer lasting effects. Evidence that high-intensity interval training may optimize benefits of exercise training is emerging. Supplemental oxygen is frequently used to manage exercise-induced desaturation, although its use as an adjunct therapy requires more evidence.SummaryCurrent evidence strongly supports the inclusion of pulmonary rehabilitation in the standard holistic care of IPF, with early participation encouraged. Further research is needed to establish the optimal exercise strategies, modalities and adjunct therapies that enhance outcomes of pulmonary rehabilitation and promote longer lasting effects.
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Soochow Univ, Med Coll, Suzhou, Peoples R China
Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Shen, Li
Zhang, Yuan
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Zhang, Yuan
Su, Yiliang
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Su, Yiliang
Weng, Dong
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Weng, Dong
Zhang, Fen
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Zhang, Fen
Wu, Qin
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Wu, Qin
Chen, Tao
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Chen, Tao
Li, Qiuhong
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Li, Qiuhong
Zhou, Ying
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Zhou, Ying
Hu, Yang
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Hu, Yang
Jiang, Xing
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Jiang, Xing
Jin, Xiaofeng
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Jin, Xiaofeng
Zhang, Aihong
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Tongji Univ, Sch Med, Dept Med Stat, Shanghai, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China
Zhang, Aihong
Li, Huiping
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Tongji Univ, Shanghai Pulm Hosp, Sch Med, Dept Resp Med, 507 Zheng Min Rd, Shanghai 200433, Peoples R ChinaSoochow Univ, Med Coll, Suzhou, Peoples R China