Incidental finding or the incognito culprit? A case of Mounier-Kuhn syndrome

被引:0
|
作者
Ozgur, Sacide S. [1 ]
Aiken, Arielle [1 ]
Bathobakae, Lefika [1 ]
Ansari, Nida [1 ]
Michael, Patrick [1 ]
Ismail, Mourad [2 ]
机构
[1] St Josephs Univ Med Ctr, Dept Med, Paterson, NJ USA
[2] St Josephs Univ Med Ctr, Dept Pulm Crit Care, Paterson, NJ USA
来源
CLINICAL CASE REPORTS | 2024年 / 12卷 / 08期
关键词
bronchiectasis; congenital tracheomegaly; lower respiratory infections; lung transplant; Mounier-Kuhn syndrome (MKS);
D O I
10.1002/ccr3.9259
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Mounier-Kuhn syndrome, characterized by tracheal dilatation due to the loss of elastic fibers and smooth muscle cells, is a rare condition, often leading to recurrent respiratory infections from impaired mucociliary clearance.
引用
收藏
页数:3
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