Benign Recurrent Intrahepatic Cholestasis: A Rare Case Report

One of the very rarely encountered causes of cholestasis is benign recurrent intrahepatic cholestasis ( BRIC). It is, usually, inherited and occasionally sporadic. It presents as recurrent relapsing and remitting cholestatic type of jaundice with normal intra and extrahepatic biliary tree. This condition, usually, benign can very rarely progress onto cirrhosis. We report an interesting case of an 18-year-old male who presented with recurrent episodes of cholestatic jaundice and pruritus, first episode beginning at 6 years of age. Imaging and liver biopsy confirmed the diagnosis of BRIC. He was managed with Rifampicin in addition to cholerectics and anti histaminics due to the initial failure in treatment response.