ACCUMULATION OF PIZ ALPHA-1-ANTITRYPSIN CAUSES LIVER-DAMAGE IN TRANSGENIC MICE

被引:241
|
作者
CARLSON, JA
ROGERS, BB
SIFERS, RN
FINEGOLD, MJ
CLIFT, SM
DEMAYO, FJ
BULLOCK, DW
WOO, SLC
机构
[1] BAYLOR COLL MED, HOWARD HUGHES MED INST, DEPT CELL BIOL, HOUSTON, TX 77030 USA
[2] BAYLOR COLL MED, HOWARD HUGHES MED INST, DEPT GASTROENTEROL, HOUSTON, TX 77030 USA
[3] BAYLOR COLL MED, HOWARD HUGHES MED INST, DEPT PATHOL, HOUSTON, TX 77030 USA
[4] BAYLOR COLL MED, INST MED GENET, HOUSTON, TX 77030 USA
来源
JOURNAL OF CLINICAL INVESTIGATION | 1989年 / 83卷 / 04期
关键词
D O I
10.1172/JCI113999
中图分类号
R-3 [医学研究方法]; R3 [基础医学];
学科分类号
1001 ;
摘要
引用
收藏
页码:1183 / 1190
页数:8
相关论文
共 50 条
  • [41] SERUM PRE-ALBUMIN LEVELS IN ALPHA-1-ANTITRYPSIN DEFICIENCY (PIZ)
    BERNINGER, RW
    BOOKER, SV
    TALAMO, RC
    METABOLISM-CLINICAL AND EXPERIMENTAL, 1982, 31 (03): : 299 - 302
  • [42] HEPATIC ACCUMULATION OF ALPHA-1-ANTITRYPSIN IN CHRONIC LIVER-DISEASE IN THE DOG
    SEVELIUS, E
    ANDERSSON, M
    JONSSON, L
    JOURNAL OF COMPARATIVE PATHOLOGY, 1994, 111 (04) : 401 - 412
  • [43] CHARACTERIZATION OF ALPHA-1-ANTITRYPSIN IN INCLUSION-BODIES FROM LIVER IN ALPHA-1-ANTITRYPSIN DEFICIENCY
    ERIKSSON, S
    JEPPSSON, JO
    LARSSON, C
    DIGESTION, 1975, 12 (4-6) : 301 - 302
  • [44] Alpha-1-antitrypsin deficiency: from genoma to liver disease. PiZ mouse as model for the development of liver pathology in human
    Giovannoni, Isabella
    Callea, Francesco
    Stefanelli, Marta
    Mariani, Riccardo
    Santorelli, Filippo M.
    Francalanci, Paola
    LIVER INTERNATIONAL, 2015, 35 (01) : 198 - 206
  • [45] ALPHA-1-ANTITRYPSIN DEFICIENCY: FROM GENOMA TO LIVER DISEASE. PiZ MOUSE AS MODEL FOR THE DEVELOPMENT OF LIVER PATHOLOGY IN HUMANS
    Giovannoni, I.
    Stefanelli, M.
    Mariani, R.
    Callea, F.
    Francalanci, P.
    JOURNAL OF HEPATOLOGY, 2013, 58 : S429 - S429
  • [46] LIVER IN NONCIRRHOTIC ALPHA-1-ANTITRYPSIN DEFICIENCY
    SHARP, HL
    MATHIS, R
    KRIVIT, W
    FREIER, E
    JOURNAL OF LABORATORY AND CLINICAL MEDICINE, 1971, 78 (06): : 1012 - &
  • [47] Decline in FEV1 in patients with PiZ alpha-1-antitrypsin deficiency:: The Australian experience
    Burdon, JGW
    Brenton, S
    Hocking, V
    Knight, KR
    Ayad, M
    Cook, L
    Janus, ED
    RESPIROLOGY, 2002, 7 (01) : 51 - 55
  • [48] Alpha-1-Antitrypsin Deficiency Liver Disease
    Patel, Dhiren
    Teckman, Jeffrey H.
    CLINICS IN LIVER DISEASE, 2018, 22 (04) : 643 - +
  • [49] ALPHA-1-ANTITRYPSIN GLOBULES IN LIVER BIOPSIES
    CLAUSEN, PP
    ACTA PATHOLOGICA ET MICROBIOLOGICA SCANDINAVICA SECTION A-PATHOLOGY, 1980, 88 (04): : 225 - 230
  • [50] WIDESPREAD EXPRESSION OF HUMAN ALPHA-1-ANTITRYPSIN IN TRANSGENIC MICE REVEALED BY INSITU HYBRIDIZATION
    KOOPMAN, P
    POVEY, S
    LOVELLBADGE, RH
    GENES & DEVELOPMENT, 1989, 3 (01) : 16 - 25