Abernethy syndrome, a rare cause of hypoxemia: A case report

被引:14
|
作者
Sahu, Manoj Kumar [1 ]
Bisoi, Akshay Kumar [1 ]
Chander, Naveen Chandrasekaran [1 ]
Agarwala, Sandeep [2 ]
Chauhan, Sandeep [3 ]
机构
[1] All India Inst Med Sci, Dept Cardiothorac & Vasc Surg, New Delhi 110029, India
[2] All India Inst Med Sci, Dept Pediat Surg, New Delhi 110029, India
[3] All India Inst Med Sci, Dept Cardiac Anesthesiol, New Delhi 110029, India
关键词
Abernethy syndrome; cyanosis; hepatopulmonary syndrome; portosystemic shunt;
D O I
10.4103/0974-2069.149526
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
Abernethy syndrome (congenital extrahepatic portosystemic shunt (CEPS II)) as an etiology of hepatopulmonary syndrome (HPS) is uncommon. The severe hypoxemia and its consequences become incapacitating for the patient. Early shunt closure resolves hypoxemia and clinical symptomatology and prevents irreversible changes in pulmonary vasculature.
引用
收藏
页码:64 / 66
页数:3
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