THROMBOSIS OF SUPERIOR LONGITUDINAL SINUS AND PULMONARY-EMBOLISM DURING A NEPHROTIC SYNDROME

被引:0
|
作者
DELMAS, MC [1 ]
COCHAT, P [1 ]
RANCHIN, B [1 ]
NEGRIER, C [1 ]
BARRE, P [1 ]
BOUVIER, R [1 ]
DAVID, L [1 ]
机构
[1] HOP EDOUARD HERRIOT,UNITE NEPHROL PEDIAT,RUE G PARRADIN,F-69008 LYONS,FRANCE
来源
PEDIATRIE | 1992年 / 47卷 / 01期
关键词
NEPHROTIC SYNDROME; THROMBOEMBOLISM; PULMONARY EMBOLISM; FACTOR-XII;
D O I
暂无
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The authors report on the case of a child with the nephrotic syndrome complicated by thrombosis of superior longitudinal sinus, bilateral massive pulmonary embolism resulting in a sudden death. A dramatic deficiency in factor XII was demonstrated; the pathophysiology and management of such an abnormality are discussed.
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页码:31 / 35
页数:5
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